Canadian Association of Radiologists Journal
Volume 63, Issue 1 , Pages 61-68, February 2012

Thoracic Computed Tomographic Manifestations of Tuberous Sclerosis in Adults

  • Amr M. Ajlan, MD

      Affiliations

    • Corresponding Author InformationAddress for correspondence: Amr M. Ajlan, MD, Department of Radiology, Vancouver General Hospital, University of British Columbia, 3350-950 West 10th Avenue, Vancouver, British Columbia V5Z 4E3, Canada.
  • ,
  • Ana Maria Bilawich, MD
  • ,
  • Nestor L. Müller, MD, PhD

Department of Radiology, Vancouver General Hospital, University of British Columbia, British Columbia, Canada

published online 09 August 2010.

Abstract 

The purpose of this article is to illustrate the various manifestations that can be encountered on thoracic computed tomography of tuberous sclerosis in adults. The pulmonary findings include lymphangioleiomyomatosis and multifocal micronodular pneumocyte hyperplasia. The extrapulmonary manifestations are divided into cardiac, vascular, mediastinal, osseous, and upper abdominal findings.

Résumé 

Le présent article vise à illustrer les diverses manifestations thoraciques de la sclérose tubéreuse observées chez des patients adultes lors d'une évaluation par tomodensitométrie. Les trouvailles pulmonaires incluent des cas de lymphangioleiomyomatose et d'hyperplasie multifocale micronodulaire des pneumocytes. Les manifestations extrapulmonaires peuvent être retrouvées parmi les catégories suivantes : cardiaque, vasculaire, médiastinale osseuse, et abdominale supérieure.

Key Words: Tuberous sclerosis, Computed tomography, Thoracic, Lymphangioleiomyomatosis, Multifocal micronodular pneumocyte hyperplasia

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PII: S0846-5371(10)00131-2

doi:10.1016/j.carj.2010.07.001

Canadian Association of Radiologists Journal
Volume 63, Issue 1 , Pages 61-68, February 2012